MODULATION OF SYNAPTIC PLASTICITY DEFICITS AS THERAPEUTIC STRATEGY IN HUNTINGTON’S DISEASE
Jordi Alberch Vié
Facultat de Medicina. Universitat de Barcelona
Isabel Pérez Otaño
Universitat Miguel Hernández. Alacant
Scientific talent responds to society for the results obtained with the donations made to La Marató
Five years ago, La Marató de TV3 and Catalunya Ràdio focused on neurodegenerative diseases with the aim of boosting research to find responses to conditions that are highly debilitating but still have no cure and the causes of which are unknown.
The slogan of that edition, "Solidarity does not degenerate" was made clear in the sum of 11.8 million euros that was raised thanks to the participation of the public on that occasion in December 2013. The 15 hours of live television led by Nuria Solé and Roger de Gràcia, and the six hours on radio hosted by Sílvia Cóppulo, were filled by the personal experiences of people who live with a neurodegenerative disease and those of their families, by contributions from doctors and researchers, by music and entertainment, and by connections with all parts of Catalonia, where members of the public took part in thousands of activities.
After that explosion of celebration and solidarity there have been years of hard, rigorous work by the 79 scientific teams that received grants to run the 44 funded research projects, of which 23 were in single centres and 21 were co-ordinated. These projects were chosen from among the 187 that responded to the invitation for applications in an evaluation process that was co-ordinated by the Catalan Agency for Health Technology Assessment and Research (AQuAS) and in which 96 international experts in neurodegenerative diseases assessed their quality, methodology, scientific, health and social relevance, innovative value and viability.
The Fundación La Marató de TV3 is now holding its 20th Symposium to present the results of this intense research activity that have been translated into new tools for prevention and of diagnosis, as well as new therapeutic approaches that improve life expectancy and quality of life of patients who have neurodegenerative diseases.
Once again the Institute of Catalan Studies is the perfect setting for the scientists who have made breakthroughs in health to meet and exchange knowledge with the society that has made them possible thanks to its support, enthusiasm, confidence and effort.
Of the 44 projects financed by La Marató 2013, more than half were co-ordinated with two or three research centres led by Catalan teams. This has boosted work by internet and the projection of the results..
MODULATION OF SYNAPTIC PLASTICITY DEFICITS AS THERAPEUTIC STRATEGY IN HUNTINGTON’S DISEASE
Jordi Alberch Vié
Facultat de Medicina. Universitat de Barcelona
Isabel Pérez Otaño
Universitat Miguel Hernández. Alacant
ROLE OF NMDA RECEPTORS PHOSPHORYLATION IN ALZHEIMER'S DISEASE AETIOLOGY: FROM PROTEOMICS TO IN VIVO MODELS
Xavier Altafaj Tardio
IDIBELL - Institut d'Investigació Biomèdica de Bellvitge. L'Hospitalet de Llobregat
SETTING A RATIONAL SCREENING PROGRAMME FOR TRANSTHYRETIN-Aβ BINDING STABILIZING COMPOUNDS THAT MAY LEAD TO POTENTIAL ALZHEIMER’S DISEASE MODULATING DRUGS
Gemma Arsequell Ruiz
Institut Química Avançada de Catalunya - CSIC. Barcelona
Isabel Cardoso
Institute for Molecular Biology and Cell Biology. Porto
Jordi Llop Roig
Asociación Centro de Investigación Coop. Biomateriales - CICbiomaGUNE. Sant Sebastià
Jesús Jiménez Barbero
CIC bioGUNE
Jordi Ramon Quintana Ruiz
Parc Científic de Barcelona - UB. Barcelona
FREEZING IN PARKINSON'S DISEASE: IMPROVING QUALITY OF LIFE WITH AN AUTOMATIC CONTROL SYSTEM
Àngels Bayés Rusiñol
Centro Médico Teknon. Barcelona
Andreu Català Mallofre
Centre Estudis Tecnològics Dependència i Vida Autònoma - UPC. Vilanova i la Geltrú
Rui Sarmento e Castro
Fraunhofer AICOS - Associaçao Fraunhofer Portugal Research- Porto
IDENTIFICATION OF SPECIFIC BIOSIGNATURES FROM PLASMA SAMPLES FOR THE DIFFERENTIAL DIAGNOSIS OF DEMENTIA WITH LEWY BODIES
Katrin Beyer
Hospital Universitari Germans Trias i Pujol - FIIGTiP
TARGETING NEURONAL DOPAMINE D1-HISTAMINE H3 RECEPTOR HETEROMERS AS A NEW TREATMENT OF HUNTINGTON’S DISEASE
Enric I. Canela Campos
Facultat de Biologia. Universitat de Barcelona
CHARACTERIZATION AND VALIDATION OF A NEW AMYLOID-β OLIGOMER AS A PHARMACOLOGICAL TARGET TO TREAT ALZHEIMER'S DISEASE
Natàlia Carulla Casanova
IRB - Institut Recerca Biomèdica de Barcelona
Serge Muyldermans
Structural Biology Research Center - VIB. Brussels (Belgium)
Giovanni Maglia
University of Leuven (Belgium)
SYSTEMS BIOMEDICINE FOR UNRAVELING THE MOLECULAR BASIS AND MODELING CORTICOSPINAL MOTOR NEURON DISEASE
Carlos Casasnovas Pons
IDIBELL - Institut d'Investigació Biomèdica de Bellvitge. L'Hospitalet de Llobregat
Maria Jesús Sobrido Gomez
FP Galega de Medicina Xenómica - Fundación Ramon Domínguez. Santiago de Compostela
Cristina Pujades Corbi
Parc de Recerca Biomèdica de Barcelona - UPF. Barcelona
Mariona Jové Font
IRBLL Institut Recerca Biomèdica de Lleida - Fundació Dr. Pifarré
CHOLESTEROL AND A-INDUCED MITOCHONDRIAL OXIDATIVE STRESS AS A CAUSAL FACTOR AND THERAPEUTIC TARGETS IN ALZHEIMER’S DISEASE
Anna Colell Riera
Institut Investigacions Biomèdiques de BCN - CSIC. Barcelona
Tobias Hartmann
Deutsches Institut für Demenzprävention DID - Saarland University. Hamburg
BILINGUALISM AS A CONTRIBUTOR TO COGNITIVE RESERVE IN HEALTHY AND PATHOLOGICAL AGEING
Albert Costa Martínez
Centre del Cervell i Cognició - UPF. Barcelona
César Avila River
Facultat de Ciències de la Salut - Universitat Jaume I. Castelló de la Plana
PRONGF/P75NTR SIGNALING IN HIPPOCAMPAL ADULT NEUROGENESIS: POTENTIAL TARGET FOR GENERATING NEW NEURONS IN ALZHEIMER’S DISEASE
Carme Espinet Mestre
IRBLL Institut Recerca Biomèdica de Lleida - Universitat de Lleida
ALZHEIMER’S DISEASE IN DOWN SYNDROME. CSF, MRI, EEG AND PET MULTIMODAL STUDIES
Juan Fortea Ormaechea
Hospital de la Santa Creu i Sant Pau - IRHSP Institut de Recerca de l'Hospital de la Santa Creu i Sant Pau
CANNABINOID RECEPTOR HETEROMERIC COMPLEXES AS THERAPEUTIC TARGETS IN PARKINSON’S DISEASE
Rafael Franco Fernández
Facultat de Biologia – Universitat de Barcelona
José Luis Lanciego Pérez
Centro de Investigación Médica Aplicada - FIMANavarra. Pamplona
DECIPHERING THE LINK BETWEEN ASTROCYTE REACTIVITY AND NEURONAL DAMAGE IN ALZHEIMER'S DISEASE
Elena Galea Rodríguez de Velasco
Institut de Neurociències – Universitat Autònoma de Barcelona
Javier Vitorica Ferrández
Facultat de Farmàcia - Universitat de Sevilla
Antonia Gutiérrez Perez
Facultat de Ciències - Universitat de Màlaga
Joan Xavier Comella Carnicé
VHIR - Institut de Recerca Hospital Universitari Vall d'Hebron
COGNITIVE TRAINING BASED ON DIGITAL MEMORIES FOR MILD COGNITIVE DETERIORATION (RE-MEMORY)
Maite Garolera Freixa
Hospital de Terrassa - Consorci Sanitari de Terrassa
PREVALENCE OF ALZHEIMER-TYPE PATHOLOGY IN NON-ALZHEIMER NEURODEGENERATIVE DISORDERS AND ITS IMPLICATION FOR THE DEVELOPMENT OF BIOMARKERS: A BRAIN-BANK-BASED POST-MORTEM STUDY
Ellen Gelpi Mantius
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
DISSECTING PROTEIN TRAFFICKING IN RETINAL NEURODEGENERATION BY SUPER-RESOLUTION IMAGING ON ANIMAL MODELS AND HUMAN IPSCS
Roser Gonzàlez Duarte
Facultat de Biologia. Universitat de Barcelona
Pablo Loza Álvarez
Fundación Pública Andaluza Progreso y Salud - CABIMER. Sevilla
Slaven Erceg
Fundación Pública Andaluza Progreso y Salud - CABIMER. Sevilla
MOLECULAR IMAGING OF THE RETINA IN PATIENTS WITH MULTIPLE SCLEROSIS BY RAMAN SPECTROSCOPY
Elena Hernández Martínez de Lapiscina
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
Pablo Loza Álvarez
ICFO - Institut de Ciències Fotòniques. Castelldefels
THERAPEUTIC IMPACT OF APOJ/CLUSTERIN-COUPLED LIPOSOMES ON ALZHEIMER'S DISEASE EXPERIMENTAL MODELS
Mar Hernández-Guillamon
VHIR - Institut de Recerca Hospital Universitari Vall d'Hebron
IDENTIFYING RELIABLE SOURCES OF STEM CELLS FOR CELL REPLACEMENT THERAPY IN RETINAL DEGENERATION DISEASES
Eloisa Herrera González de Molina
Institut de Neurociències d'Alacant - CSIC. Sant Joan d'Alacant
Marta Agudo Barriuso
Instituto Murciano de Investigación Biosanitaria Virgen de la Arrixaca –
Fundación para la Formación e Investigación Sanitaria
ROLE OF IL-6 TRANS-SIGNALING IN A MOUSE MODEL OF ALZHEIMER’S DISEASE
Juan Hidalgo Pareja
Facultat de Biociències. Universitat Autònoma de Barcelona
BRAIN CONNECTIVITY CHANGES DURING THE DEGENERATIVE PROCESS IN PARKINSON’S DISEASE
Carme Junqué Plaja
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
PREDICTION OF APATHY AND IMPULSE CONTROL DISORDERS IN PARKINSON'S DISEASE BASED ON THE FEEDBACK RELATED NEGATIVITY (FRN), A NEUROPHYSIOLOGICAL MARKER OF INCENTIVE PROCESSING
Jaume Kulisevsky Bojarski
Institut Recerca Hospital de l'Hospital de la Santa Creu i Sant Pau
NEW TECHNOLOGIES APPLIED TO CLINICAL PRACTICE FOR OBTAINING BIOMARKERS OF ATROPHY AND LESIONS IN MAGNETIC RESONANCE IMAGES OF PATIENTS WITH MULTIPLE SCLEROSIS (BIOMARKEM.CAT)
Xavier Lladó Bardera
Escola Politècnica Superior - Universitat de Girona
Jordi Rio Izquierdo
Centre d'Esclerosi Múltiple de Catalunya CEMCAT - Institut de Recerca de la Vall d'Hebron
Joan Carles Vilanova Busquets
Institut Hospital Dr. Josep Trueta Girona - IDIBGI
SYNAPTIC MARKERS IN PRECLINICAL ALZHEIMER'S DISEASE
Alberto Lleó Bisa
Hospital de la Santa Creu i Sant Pau - Institut de Recerca HSCiSP
CATALAN NETWORK OF MULTIPLE SYSTEM ATROPHY: BIOMARKERS AND PATHOPHYSIOLOGY
Josefa Maria Martí Domènech
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
Gian Gaetano Tartaglia
Centre de Regulació Genòmica
GENE THERAPY TARGETING NEUREGULIN FOR THE TREATMENT OF AMYOTROPHIC LATERAL SCLEROSIS
Xavier Navarro Acebes
Facultat de Medicina - Universitat Autònoma de Barcelona
PLASMA AND NEUROPHYSIOLOGICAL MARKERS OF THE PROGRESSION OF COGNITIVE IMPAIRMENT TO PARKINSON'S DISEASE
Javier Pagonabarraga Mora
Hospital de la Santa Creu i Sant Pau - Institut de Recerca HSCiSP
CATALAN ADAPTATION AND NORMALITZATION OF NEUROPSYCHOLOGICAL INSTRUMENTS
Jordi Peña Casanova
IMIM - Institut Hospital del Mar d'Investigacions Mèdiques
NEURODEGENERATION WITH BRAIN IRON ACCUMULATION (NBIA) DISORDERS: CLINICAL EVALUATION AND GENETIC CHARACTERISATION THROUGH A SPANISH MULTICENTRE RESEARCH NETWORK
Belén Pérez Dueñas
VHIR Institut de Recerca Hospital Universitari Vall d'Hebron
Carmen Espinós Armero
Centro de Investigación Príncipe Felipe - CIBERER. València
IMPACT OF OBSTRUCTIVE SLEEP APNEA IN THE EVOLUTION OF ALZHEIMER DISEASE. ROLE OF HYPOXIA AND SLEEP FRAGMENTATION
Gerard Piñol Ripoll
Hospital de Santa Maria - Institut de Recerca Biomèdica Fundació Dr. Pifarré Lleida
Ramon Farré Ventura
Facultat de Medicina. Universitat de Barcelona
David Gozzal
University of Chicago Medical Center
THE ROLE OF REELIN AT THE CROSSROADS OF ALZHEIMER'S DISEASE MECHANISMS: TAUOPATHY, AMYLOID TOXICITY AND TRANSMISSIBILITY
Lluís Pujadas Puigdomènech
VHIR Institut de Recerca Hospital Universitari Vall d'Hebron
José María Delgado García
Facultad de ciencias experimentales / Universidad Pablo de Olavide
CHARACTERIZATION OF NOVEL SUPPRESSORS OF NEURONAL TOXICITY IN MYOTONIC DYSTROPHY TYPE 1
Patricia Robledo Montoya
IMIM - Institut Hospital del Mar d'Investigacions Mèdiques. Barcelona
Manuel Pérez Alonso
Institut de Recerca Sanitària. València
SEARCHING NEW BIOMARKERS AND THERAPEUTIC TARGETS RELATED TO COGNITIVE DEFICITS IN EARLY STAGES OF ALZHEIMER'S DISEASE: ROLE OF AKAP79/150, CPT1C AND SSAO/VAP-1 IN Aβ-MEDIATED AMPAR DYSFUNCTION
José Rodríguez Álvarez
Institut de Neurociències. Universitat Autònoma de Barcelona
BIOMARKERS PROFILE IN DIFFERENT MOTOR NEURON DISEASE PHENOTYPES
Ricardo Rojas Garcia
Hospital de la Santa Creu i Sant Pau - Institut de Recerca HSCiSP
DIAGNOSTIC AND PROGNOSTIC BIOMARKERS IN PEDIATRIC MULTIPLE SCLEROSIS AND RELATED DEMYELINATING DISORDERS
Albert Saiz Hinarejos
Hospital Clínic i Provincial de Barcelona. Fundació Clínic per a la Recerca Biomèdica
Mar Tintoré Subirana
VHIR - Institut de Recerca Hospital Universitari Vall d'Hebron
STUDY OF GENETIC FRONTOTEMPORAL DEMENTIA IN PRECLINICAL AND EARLY STAGES OF THE DISEASE: COGNITIVE PERFORMANCE, STRUCTURAL AND FUNCTIONAL NEUROIMAGING AND BIOCHEMICAL MARKERS
Raquel Sánchez del Valle Díaz
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
ICTAL SPECT IN THE PARKINSON PREMOTOR PHASE OF STUDY
Joan Santamaria Cano
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
NEW STEM CELL THERAPIES FOR DUCHENE MUSCULAR DYSTROPHY
Antonio L. Serrano Sánchez
Facultat Ciències Salut i Vida – UPF, Barcelona
Francesco Saverio Tedesco
Cell and Developmental Biology - University College, London
Giulio Cossu
Centre For Tissue Injury and Repair - University of Manchester (UK)
MRI BRAIN CONNECTOMICS AND METABOLIC IMAGING IN THE TGF344-AD RAT: A NEW APPROACH FOR THE STUDY OF ALZHEIMER'S DISEASE
Guadalupe Soria Rodríguez
IDIBAPS - Institut d'Investigació Biomèdica August Pi i Sunyer
PRECLINICAL TESTING OF DRUGS AGAINST THE TOXIC EFFECTS OF MUTANT HUNTINGTIN IN MURINE MODELS OF HD
Rafael Vázquez-Manrique
Hospital Universitari i Politècnic La Fe. València
DECIPHERING THE ROLE OF ALPHA-SYNUCLEIN STRAINS IN PRION-LIKE SYNUCLEINOPATHY INDUCTION AND SPREADING
Salvador Ventura Zamora
Institut Biotecnologia i Biomedicina – UAB, Bellaterra
Tiago Outeiro
University Medical Center Göttingen (Alemanya)
Juan Maria Torres Trillo
Centro de Investigación en Sanidad Animal - Instituto Nacional de Investigación y Tecnologia Agraria y Alimentaria. Valdeolmos (Madrid)
EVALUATION OF AN INNOVATIVE INTERVENTION (INFORMATIVE, FORMATIVE AND OF SOCIAL SUPPORT) "INFOSA-DEM" TO INFORMAL CAREGIVERS OF PEOPLE WITH DEMENTIA LIVING AT HOME
Adelaida Zabalegui Yárnoz
Hospital Clínic i Provincial de Barcelona - Fundació Clínic per a la Recerca Biomèdica